Chicago – September 18, 2026 -- The American Lung Association has launched a national campaign to help patients and caregivers recognize the early warning signs of progressive pulmonary fibrosis (PPF), timed to World Interstitial Lung Disease Day.
PPF describes worsening lung scarring that can occur in people living with an interstitial lung disease (ILD), a group of more than 200 conditions that cause inflammation or scarring of the lungs. Harold Wimmer, President and CEO of the American Lung Association, said the causes range from autoimmune diseases to environmental or occupational exposures, or remain unknown, but all share the risk that scarring can worsen over time.
Doctors watch for three specific signs to confirm PPF
PPF is not itself a disease but a pattern of decline. It is diagnosed when at least two of three signs appear together: worsening symptoms, a drop in lung function on breathing tests, and increased scarring visible on a high-resolution CT scan.
Early warning signs include worsening shortness of breath, unusual fatigue and unintentional weight loss. The Lung Association says these symptoms should prompt a conversation with a medical specialist as soon as possible.
Treatment options include antifibrotic medicines and oxygen support
Depending on the specific ILD, treatment may involve medicines that reduce inflammation, suppress the immune system, or slow scarring. Antifibrotic medicines have been shown to slow the loss of lung function, while supportive care can include supplemental oxygen, pulmonary rehabilitation or palliative care.
George Savich, who lives with pulmonary fibrosis, said patients need reliable information about treatment options, disease management and where to find support.
Free navigators and a 50-page workbook are now available
The campaign expands free access to the Lung Association's Lung Health Navigator program, staffed by registered nurses and respiratory therapists who offer one-on-one education in English and Spanish. Participating patients and caregivers will receive a 50-page "Learning to Live with PF" workbook by mail, covering communication tips for healthcare visits, symptom management, nutrition and physical activity guidance.
Support for the campaign was provided by Boehringer Ingelheim.